DisorderVariants
Diffuse cutaneous systemic sclerosis
Limited cutaneous systemic sclerosisCREST syndrome
Systemic sclerosis sine scleroderma
Localized sclerodermaLinear scleroderma
En coup de saber
Morphea
Generalized
Plaque
Mixed connective tissue diseaseFeatures of systemic sclerosis, polymyositis, and SLE
Overlap syndromesSystemic sclerosis plus polymyositis, rheumatoid arthritis, or SLE
Scleroderma mimicsAmyloidosis
Chronic graft-versus-host disease
Diffuse fasciitis with eosinophilia
Eosinophilia-myalgia syndrome
Nephrogenic fibrosing dermopathy
Paraneoplastic syndromes
Scleredema
Scleromyxedema (papular mucinosis)
Toxic oil syndrome
Undifferentiated connective tissue diseaseMultiple nonspecific, serologic or clinical abnormalities that do not meet ACR criteria for rheumatic disease