DiagnosisInitial testsAdditional tests
VWF:RCo (IU per dL)*VWF:Ag (IU per dL)*Factor VIIIRatio of VWF: RCo to VWF:AgRIPAVWF multimers
Type 1< 30< 30↓ or normal> 0.5 to 0.7Often normalNormal
Type 2A< 30< 30 to 200↓ or normal< 0.5 to 0.7↓ high-molecular-weight multimers
Type 2B< 30< 30 to 200↓ or normalUsually < 0.5 to 0.7↓ high-molecular-weight multimers
Type 2M< 30< 30 to 200↓ or normal< 0.5 to 0.7Normal
Type 2N30 to 20030 to 200↓ ↓> 0.5 to 0.7NormalNormal
Type 3< 3< 3↓ ↓ ↓ (< 10 IU per dL)NAAbsentNA
Low VWF30 to 50§30 to 50§Normal> 0.5 to 0.7NormalNormal
Normal50 to 20050 to 200Normal> 0.5 to 0.7NormalNormal