ConditionDescriptionvWF:RCo (IU per dL)vWF:Ag (IU per dL)Ratio of vWF:RCo to vWF:AgFactor VIII
Type IPartial quantitative deficiency vWF< 30< 30> 0.5 to 0.7Normal or low
Type 2ADecreased vWF-dependent platelet adhesion with selective deficiency of high–molecular-weight multimers< 30< 30 to 200*< 0.5 to 0.7Normal or low
Type 2BIncreased affinity for platelet glycoprotein Ib< 30< 30 to 200*Usually < 0.5 to 0.7Normal or low
Type 2MDecreased vWF-dependent platelet adhesion without selective deficiency of high–molecular-weight multimers< 30< 30 to 200*< 0.5 to 0.7Normal or low
Type 2NMarkedly decreased binding affinity for factor VIII30 to 20030 to 200> 0.5 to 0.7Very low
Type 3Virtually complete quantitative deficiency of vWF< 3< 3NAExtremely low (< 10 IU per dL)
Low vWFBorderline deficiencies30 to 5030 to 50> 0.5 to 0.7Normal
NormalNA50 to 20050 to 200> 0.5 to 0.7Normal